A Rare Case of Bilateral Microspherophakia

Abstract

Microspherophakia is a rare bilateral congenital anomaly of the crystalline lens. The condition may be isolated, familial, or it may be associated with systemic affections like Marfan’s syndrome, Weil-Marchesani syndrome, hyperlysinemia and congenital rubella. Microspherophakia results in lenticular myopia, lens dislocation, usually inferiorly and inverse glaucoma. We present a case in a 8 year old child who presented with bilateral microspherophakia. Visual acuity in the right eye was counting fingers close to face and in the left eye 6/60.IOP with Perkins applanation tonometer was 30 mmHg in the right eye and 22 mmHg in the left eye, cornea was hazy due to edema, anterior chamber was shallow in both eye patient was managed with emergency lens extraction of the right eye and secondary ACIOL implantation. Left eye was managed by laser peripheral iridotomy. IOP was within normal limits postoperatively in both eyes without any antiglaucoma medications. Postoperatively, best corrected visual acuity in the right eye was 6/18 and 6/9 in the left eye.